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KMID : 0942820070060010039
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Journal of Korean Brain Tumor Society
2007 Volume.6 No. 1 p.39 ~ p.43
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Conservative Management and Radiation Therapy of Gorham’s Disease Involved Skull Base and upper Cervical Spine - Case Report -
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Jang In-Seok
Park Jun-Bum
Ra Young-Shin
Kim Jeong-Hoon
Koo Hyun-Lyoung
Kang Shin-Kwang
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Abstract
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A 10-year-old boy was admitted at our institute with neck pain, limiting the neck movement and chin point deviation to the right. Which confirmed the suspected diagnosis of Gorham’s disease, the patient underwent biopsy on the 3rd cervical spine. Gorham’s disease was confidently diagnosed with the support of present clinical and radiographic findgings by a regional histopathologist. In order to diminish neck pain and ensure radiation field uniformity, a halo-vest was recommended. The patient received 4,000 cGy of radiation to the upper cervical osteolytic lesion. There has been no radiographic evidence of progression of the disease at the MR follow-up of post-radiotherapy 23 months. At present, the patient is remarkably doing well with no evidence of disease progression. The authors suggest that application of a halo-vest and early radiation therapy can be a good choice to management of Gorham’s disease involving skull base and upper cervical spine. However, long term follow-up will be essential to confirm the remission of disease.
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KEYWORD
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Gorham disease, Osteolysis, essential, Skull base, Cervical vertebrae, Radiation therapy, Halo-vest
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